Congenital Hepatic Fibrosis (CHF) is a rare, congenital, inherited disorder. The cause is thought to be a faulty gene, which affects the way in which the liver and bile ducts are formed. The bile ducts may be dilated and have an abnormal structure. The liver may have large bands of fibrous (scar) tissue.
The rate of bile duct damage varies from patient to patient, as does the rate of fibrosis formation. If the fibrosis continues to worsen, the liver may become firmer, making it more difficult for the blood to flow through it. CHF can also be associated with other conditions which can affect the liver and kidneys and can also be accompanied by abnormalities in the portal vein and, less commonly, in other blood vessels supplying the brain and the heart.
Download CLDF’s leaflet on congenital hepatic fibrosis.
You can also order a copy of the leaflet here.
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