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Home Information Medical stuff Information on liver diseases Congenital Hepatic Fibrosis

Congenital Hepatic Fibrosis

About congenital hepatic fibrosis

Congenital hepatic fibrosis (CHF) is a rare, congenital, inherited disorder. The cause is thought to be a faulty gene, which affects the way in which the liver and bile ducts are formed. The bile ducts may be dilated and have an abnormal structure. The liver may have large bands of fibrous (scar) tissue.

The rate of bile duct damage varies from patient to patient, as does the rate of fibrosis formation. If the fibrosis continues to worsen, the liver may become firmer, making it more difficult for the blood to flow through it. CHF can also be associated with other conditions which can affect the liver and kidneys and can also be accompanied by abnormalities in the portal vein and, less commonly, in other blood vessels supplying the brain and the heart.

Want to know more?

Download CLDF’s leaflet on congenital hepatic fibrosis.

You can also order a copy of the leaflet here.

The information on this site is for guidance only. It is not a substitute for professional medical care by a qualified doctor or other health care professional. ALWAYS check with your medical team if you have any concerns about your condition or treatment. CLDF is not responsible or liable, directly or indirectly, for any form of damages resulting from the use (or misuse) of information contained in or implied by the information on this site.